Background Mucous membrane pemphigoid (MMP), also known as cicatricial pemphigoid, is a serious, autoimmune, blistering disorder that can result in blindness and other complications as a result of scarring of the mucous membranes. Effective treatment modalities are often toxic.
Historically, the term "cicatricial pemphigoid" also referred to MMP. Although both bullous pemphigoid and MMP may affect skin and mucosa, the classical clinical findings in bullous pemphigoid are tense, fluid-filled bullae on skin, whereas the prevailing clinical feature in MMP is mucosal involvement.
L12. 0 is a billable/specific ICD-10-CM code that can be used to indicate a diagnosis for reimbursement purposes. The 2022 edition of ICD-10-CM L12.
Cicatricial pemphigoid is a rare, chronic autoimmune blistering disorder which can produce scarring. It can affect the skin only, mucous membranes only, or both the skin and mucous membranes. When only mucous membranes are involved, the disease is often referred to as mucous membrane pemphigoid.
Pemphigus is characterized by shallow ulcers or fragile blisters that break open quickly. Pemphigoid presents with stronger or “tense” blisters that don't open easily. Those with pemphigoid are also more likely to have hot, red and itchy hive spots.
All types of pemphigoid are caused by your immune system attacking healthy tissue. They appear as rashes and fluid-filled blisters. The types of pemphigoid differ in terms of where on the body the blistering occurs and when it occurs.
ICD-10 code L12. 0 for Bullous pemphigoid is a medical classification as listed by WHO under the range - Diseases of the skin and subcutaneous tissue .
Causes of bullous pemphigoid Bullous pemphigoid is caused by a problem with the immune system (the body's defence against infection). Instead of attacking germs, it attacks and damages the skin. It's not known why this happens. Sometimes it's been linked to skin damage (such as sunburn) or taking certain medicines.
2022 ICD-10-CM Diagnosis Code L10: Pemphigus.
Mucous membranes line many tracts and structures of the body, including the mouth, nose, eyelids, trachea (windpipe) and lungs, stomach and intestines, and the ureters, urethra, and urinary bladder.
(MYOO-kus MEM-brayn) The moist, inner lining of some organs and body cavities (such as the nose, mouth, lungs, and stomach). Glands in the mucous membrane make mucus (a thick, slippery fluid). Also called mucosa.
Stomatitis is inflammation of the mucous membrane of the mouth, including the inner aspect of the lips, cheeks, gums, tongue, and throat. It is a type of mucositis.
(MYOO-kus MEM-brayn) The moist, inner lining of some organs and body cavities (such as the nose, mouth, lungs, and stomach). Glands in the mucous membrane make mucus (a thick, slippery fluid). Also called mucosa.
Lesions between the two diseases look different. Pemphigus vulgaris lesions have flaccid bullae, erosions, and flexural vegetations or growths, and bullous pemphigoid has urticated plaques, tense bullae, and some milia.
Stomatitis is a type of mucositis, a condition defined as pain or inflammation of the mucous membrane. Mucositis is a relatively common side effect of chemotherapy and sometimes radiotherapy. It can affect the inside of the lips, cheeks, gums, tongue, and throat.
Bullous pemphigoid is most common in older adults. Bullous pemphigoid occurs when your immune system attacks a thin layer of tissue below your outer layer of skin. The reason for this abnormal immune response is unknown, although it sometimes can be triggered by taking certain medications.