Disease definition. Early onset cerebellar ataxia with retained reflexes (EOCARR) or Harding ataxia is a cerebellar ataxia characterized by the progressive association of a cerebellar and pyramidal syndrome with progressive cerebellar ataxia, brisk tendon reflexes, and sometimes profound sensory loss.
81 for Cerebellar ataxia in diseases classified elsewhere is a medical classification as listed by WHO under the range - Diseases of the nervous system .
Spinocerebellar ataxia type 1 (SCA1) is a condition characterized by progressive problems with movement. People with this condition initially experience problems with coordination and balance (ataxia).
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Pravin Khemani, MD. The ataxias are clinically heterogenous disorders caused by pathological processes affecting the cerebellum and cerebellar pathways resulting in impaired coordination.
Acute cerebellar ataxia is sudden, uncoordinated muscle movement due to disease or injury to the cerebellum. This is the area in the brain that controls muscle movement. Ataxia means loss of muscle coordination, especially of the hands and legs.
SCA is hereditary, progressive, degenerative, and often fatal. There is no known effective treatment or cure. SCA can affect anyone of any age. The disease is caused by either a recessive or dominant gene....Spinocerebellar ataxiaCerebellum (in blue) of the human brainSpecialtyNeurology2 more rows
Ataxia is a degenerative disease of the nervous system. Many symptoms of Ataxia mimic those of being drunk, such as slurred speech, stumbling, falling, and incoordination. These symptoms are caused by damage to the cerebellum, the part of the brain that is responsible for coordinating movement.
Many hereditary ataxias, including most of the more common SCAs, manifest significant central nervous system involvement beyond the cerebellum to the brainstem and spinal cord, hence the designation “spinocerebellar” ataxia (3, 8).
Compared with Bell's palsy (facial paralysis without rash), patients with Ramsay Hunt syndrome often have more severe paralysis at onset and are less likely to recover completely.
Ramsay Hunt syndrome type 2 is caused by reactivation of varicella zoster virus in the geniculate ganglion. Patient often presents with facial nerve paralysis leading to facial droop, dry eyes, mouth and hearing loss.
Ramsay Hunt syndrome is a painful rash around the ear, on the face, or on the mouth. It occurs when the varicella-zoster virus infects a nerve in the head.