icd-10 code for focal segmental glomerulosclerosis

by Lorenz Lehner 6 min read

1 for Nephrotic syndrome with focal and segmental glomerular lesions is a medical classification as listed by WHO under the range - Diseases of the genitourinary system .

What is focal segmental glomerulosclerosis?

Focal segmental glomerulosclerosis is scar tissue in the filtering unit of the kidney. This structure is called the glomerulus. The glomeruli serve as filters that help the body get rid of harmful substances. Each kidney has thousands of glomeruli. "Focal" means that some of the glomeruli become scarred.

Is Focal segmental glomerulosclerosis a chronic kidney disease?

FSGS is a chronic disease, because the scarred glomeruli cannot be repaired. Treatment can slow the process of kidney disease.

Is Focal segmental glomerulosclerosis a nephrotic syndrome?

FSGS is a rare disease that attacks the kidney's filtering units (glomeruli) and causes serious scarring, leading to permanent kidney damage and even kidney failure. FSGS is one of the causes of a serious condition known as Nephrotic Syndrome.

What is secondary focal segmental glomerulosclerosis?

Focal segmental glomerulosclerosis (FSGS) is a common cause of proteinuria and nephrotic syndrome leading to end stage renal disease (ESRD). There are two types of FSGS, primary (idiopathic) and secondary forms. Secondary FSGS shows less severe clinical features compared to those of the primary one.

Why is segmental glomerulosclerosis called focal?

Focal segmental glomerulosclerosis (FSGS) is a rare disease that received its name because of how the affected kidney tissue looked under a microscope. Each of your kidneys contain about one million small filters. These filters are made up of a tuft of small blood vessels called a glomerulus.

How many types of FSGS are there?

Another classification system, called the Columbia Classification, breaks down FSGS into five subtypes based on the appearance (morphology) of the FSGS lesions affecting the glomeruli as seen under a microscope. These five variants are: perihilar, cellular, tip, collapsing, and FSGS not otherwise specified.

Is Focal segmental glomerulosclerosis an autoimmune disease?

FSGS can be a result of an autoimmune disease, in which the body attacks itself without cause, or the result of a pre-existing medical condition such as the following: Kidney defects from birth. Urine back-ups in the kidney.

What is the difference between primary and secondary FSGS?

Primary FSGS was defined as having diffuse FPE without an identifiable cause. Patients who had limited FPE, or had diffuse FPE but had an identifiable cause for FPE were classified as secondary FSGS.

Is FSGS a terminal illness?

It is a scarring disease of the kidney that generally causes excess protein in the urine, nephrotic syndrome, and progressive kidney failure. It is not fatal, as dialysis and transplant would be the treatment of choice for FSGS that progresses to kidney failure.

What is recurrent FSGS?

Focal segmental glomerulosclerosis (FSGS) is a common cause of end-stage renal disease and a common pathologic diagnosis of idiopathic nephrotic syndrome (NS), especially in steroid-resistant cases. FSGS is known to recur after kidney transplantation, frequently followed by graft loss.

The ICD code N041 is used to code Focal segmental glomerulosclerosis

Focal segmental glomerulosclerosis (FSGS) is a cause of nephrotic syndrome in children and adolescents, as well as an leading cause of kidney failure in adults. It is also known as "focal glomerular sclerosis" or "focal nodular glomerulosclerosis." It accounts for about a sixth of the cases of nephrotic syndrome.

Coding Notes for N04.1 Info for medical coders on how to properly use this ICD-10 code

Inclusion Terms are a list of concepts for which a specific code is used. The list of Inclusion Terms is useful for determining the correct code in some cases, but the list is not necessarily exhaustive.

MS-DRG Mapping

DRG Group #698-700 - Other kidney and urinary tract diagnoses with MCC.

ICD-10-CM Alphabetical Index References for 'N04.1 - Nephrotic syndrome with focal and segmental glomerular lesions'

The ICD-10-CM Alphabetical Index links the below-listed medical terms to the ICD code N04.1. Click on any term below to browse the alphabetical index.

Equivalent ICD-9 Code GENERAL EQUIVALENCE MAPPINGS (GEM)

This is the official approximate match mapping between ICD9 and ICD10, as provided by the General Equivalency mapping crosswalk. This means that while there is no exact mapping between this ICD10 code N04.1 and a single ICD9 code, 581.1 is an approximate match for comparison and conversion purposes.

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