Short description: Sicca syndrome [Sjogren] The 2021 edition of ICD-10-CM M35.0 became effective on October 1, 2020. This is the American ICD-10-CM version of M35.0 - other international versions of ICD-10 M35.0 may differ. The following code (s) above M35.0 contain annotation back-references.
Short description: Sicca syndrome [Sjogren] The 2019 edition of ICD-10-CM M35.0 became effective on October 1, 2018.
Sicca syndrome [Sjögren] The disease causes dry eyes and mouth, and may cause dryness in the nose, throat, air passages, skin, and vagina. It may also cause inflammation in the joints, muscles, and skin; pneumonia; tingling in the fingers and toes; and fatigue. It often occurs with rheumatoid arthritis or other connective tissue diseases.
Nine of 10 are women. Sjogren's syndrome is sometimes linked to rheumatic problems such as rheumatoid arthritis.sjogren's syndrome is an autoimmune disease. If you have an autoimmune disease, your immune system, which is supposed to fight disease, mistakenly attacks parts of your own body.
There are two forms of Sjögren's syndrome:Primary Sjögren's syndrome develops on its own, not because of any other health condition.Secondary Sjögren's syndrome develops in addition to other autoimmune diseases like rheumatoid arthritis, lupus and psoriatic arthritis.
Sjogren's (SHOW-grins) syndrome is a disorder of your immune system identified by its two most common symptoms — dry eyes and a dry mouth. The condition often accompanies other immune system disorders, such as rheumatoid arthritis and lupus.
Rheumatoid arthritis (RA) is frustrating enough on its own. But about 15 percent of people with RA develop a complication that affects the tear and saliva glands, causing dry mouth, dry eyes, dry skin, and additional symptoms that further aggravate their arthritis. It's called Sjögren's syndrome (SS).
Primary Sjogren syndrome is an autoimmune condition in which dry eyes (keratoconjunctivitis sicca) and dry mouth (xerostomia) result from lymphocytic infiltration of lacrimal and salivary glands.
Causes of Sjögren's syndrome Sjögren's syndrome is caused by the immune system (the body's defence against infection), damaging healthy parts of the body. This is known as an autoimmune condition. The condition usually affects areas of the body that produce fluids, such as tears and saliva.
In secondary Sjogren's syndrome, which accounts for over 50% of the cases diagnosed, other autoimmune diseases are present, including rheumatoid arthritis (20-30%), systemic lupus erythematosus (15-35%), systemic sclerosis (10-25%), and psoriatic arthritis.
Most often, the co-occurring autoimmune disease is rheumatoid arthritis. Other individuals with secondary Sjogren's may have lupus, scleroderma, primary biliary cirrhosis, or a different kind of autoimmune disease.
Sjogren's is a serious condition, but timely treatment can mean that complications are less likely to develop, and tissue damage is less likely to occur. Once treated, an individual can usually manage the condition well. Sjogren's can develop at any age, but most diagnoses occur after the age of 40 years.
Treat systemwide symptoms. Hydroxychloroquine (Plaquenil), a drug designed to treat malaria, is often helpful in treating Sjogren's syndrome. Drugs that suppress the immune system, such as methotrexate (Trexall), also might be prescribed.
Primary Sjögren syndrome occurs in the absence of another underlying rheumatic disorder, whereas secondary Sjögren syndrome is associated with another underlying rheumatic disease, such as systemic lupus erythematosus (SLE), rheumatoid arthritis (RA), or scleroderma.
Life expectancy and primary Sjogren's syndrome Life expectancy in primary Sjogren's syndrome is comparable to that of the general population, but it can take up to seven years to correctly diagnose Sjogren's. Although life expectancy is not typically affected, patients' quality of life is, and considerably.
Sjogren's syndrome can occur alone or in association with other autoimmune diseases, most commonly lupus and rheumatoid arthritis (RA). Several studies have shown various differences between people with SS alone and those with SS and another connective tissue disease.
An initiative to revise and update the ICD-10 Code for Sjögren’s, which began in 2017 , was coordinated and led by the Sjögren’s Foundation, in partnership with the American College of Rheumatology and with the help and input from a group of multi-specialty experts.
While dryness (sicca) certainly occurs in Sjögren’s, dryness alone does not represent the disease and its many other manifestations. Multiple years of planning and presenting to government agencies has resulted in a revised ICD-10 code for Sjögren’s, which is set to take effect in October 2020.
We, and many others knew that Sjögren’s and sicca are not synonymous, with sicca being a symptom but not a disease, and Sjögren’s being a distinct systemic autoimmune rheumatic disease that can affect multiple organs and body systems.