Other diseases of capillaries 2016 2017 2018 2019 2020 2021 Billable/Specific Code I78.8 is a billable/specific ICD-10-CM code that can be used to indicate a diagnosis for reimbursement purposes. The 2021 edition of ICD-10-CM I78.8 became effective on October 1, 2020.
Capillary malformation (CM) is a type of vascular anomaly, which is an anomaly or disorder of the vascular system, either in veins or arteries. CMs are commonly known as port wine stains.
If you look at the Index in your ICD-9-CM book under Malformation, go to Chiari. It lists for you type 1-4 and the respective codes. Always be sure to verify in the Tabular List.
This is the American ICD-10-CM version of Q89.9 - other international versions of ICD-10 Q89.9 may differ. Any abnormality, anatomical or biochemical, evident at birth or during the neonatal period. Malformations of organs or body parts during development in utero.
Capillary malformation (CM) is a type of vascular anomaly, which is an anomaly or disorder of the vascular system, either in veins or arteries.
A doctor will diagnose a CM by examining the mark and asking questions about the patient’s history. For simple CMs, other imaging studies are not needed to diagnose them.
Most CMs cannot be cured, but there are ways to treat and manage this condition.
Various sets of criteria have been suggested to identify the disorder in an individual patient, all of which include macrocephaly and a number of the following: somatic overgrowth, cutis marmorata, midline facial birthmark, polydactyly/syndactyly, asymmetry (hemihyperplasia or hemihypertrophy), hypotonia at birth, developmental delay, connective tissue defect and frontal bossing. Currently no consensus exists about which diagnostic criteria are definitive and so evaluation by a medical geneticist or other clinician with familiarity with the syndrome is usually needed to provide diagnostic certainty. It is not clear if there are some features which are mandatory to make the diagnosis, but macrocephaly appears essentially universal though may not be congenital. The distinctive vascular abnormalities of the skin often fade over time, making the diagnosis challenging in older children with this condition.
There is no cure for this condition. Treatment is supportive and varies depending on how symptoms present and their severity. Some degree of developmental delay is expected in almost all cases of M-CM, so evaluation for early intervention or special education programs is appropriate. Rare cases have been reported with no discernible delay in academic or school abilities.
Mosaic mutations in PIK3CA have been found to be the genetic cause of M-CM. Other overgrowth conditions with distinct phenotypes have also been found to be caused by mosaic mutations in PIK3CA. How different mutations in this gene result in a variety of defined clinical syndromes is still being clarified. Mutations in PIK3CA have not been found in a non-mosaic state in any of these disorders, so it is unlikely that the conditions could be inherited.
It is not clear if there are some features which are mandatory to make the diagnosis, but macrocephaly appears essentially universal though may not be congenital. The distinctive vascular abnormalities of the skin often fade over time, making the diagnosis challenging in older children with this condition.