icd 9 code for juvenile xanthogranuloma

by Clark Willms 8 min read

Short description: Benign neo skin eyelid. ICD-9-CM 216.1 is a billable medical code that can be used to indicate a diagnosis on a reimbursement claim, however, 216.1 should only be used for claims with a date of service on or before September 30, 2015.

What is the ICD-10-CM diagnosis code for xanthogranuloma 1?

Jul 18, 2013 · What is the correct ICD-9-CM code for juvenile xanthogranuloma? Answer: Assign code 216.X Benign neoplasm of skin, for juvenile xanthogranuloma, with the appropriate 4th digit to specify the site. This condition is not a systemic metabolic disorder and affected persons have normal lipid metabolism. Juvenile xanthogranuloma is a benign cutaneous histiocytic …

What is juvenile xanthogranuloma?

Jul 25, 2018 · 400031009 – Juvenile xanthogranuloma Look For. Subscription Required. Diagnostic Pearls. Subscription Required. Differential Diagnosis & Pitfalls The primary differential of red-to-yellow papules on a young child is JXG, Spitz nevus, and mastocytoma. Mastocytomas – Similar in color to JXGs, but they urticate when rubbed.

What is the ICD 9 code for diagnosis?

Aug 11, 2021 · Juvenile xanthogranuloma (JXG) is a relatively common entity and is the most common form of non-Langerhans cell histiocytic disorder of childhood.[1], [2] It is estimated that in 75% of cases, lesions appear during the first year of life, with >15-20% of patients having lesions at birth. JXG is rare in adults, with a peak incidence in the late twenties to thirties. …

What is the clinical presentation of xanthoma multiplex?

May 24, 2021 · Nevoxanthoendothelioma, xanthoma multiplex, juvenile xanthoma, multiple eruptive xanthoma in infancy, congenital xanthoma tuberosum, xanthoma neviforme and juvenile giant cell granuloma ICD coding ICD-10: D76.3 - Other histiocytosis syndromes

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Synopsis

Juvenile xanthogranulomas (JXG) are benign, spontaneously regressing histiocytic tumors of unknown pathogenesis. The incidence is unknown, and there may be a slight male preponderance.

Differential Diagnosis & Pitfalls

The primary differential of red-to-yellow papules on a young child is JXG, Spitz nevus, and mastocytoma.

What is JXG in medical terms?

Essential features. Juvenile xanthogranuloma (JXG) is a rare, benign proliferative non-Langerhans cell histiocytic proliferation. Occurs predominantly in young children. Clinically, it presents as a solitary red-brown, yellowish papule or nodule, most often on the head and neck area. Systemic JXG is rare and may involve any organ system.

What is a JXG?

Juvenile xanthogranuloma (JXG) is a rare, benign proliferative non-Langerhans cell histiocytic proliferation. Occurs predominantly in young children. Clinically, it presents as a solitary red-brown, yellowish papule or nodule, most often on the head and neck area. Systemic JXG is rare and may involve any organ system.

Other names for juvenile xanthogranuloma

Juvenile xanthogranuloma (JXG) has also been called naevoxanthoendothelioma, xanthoma multiplex, juvenile xanthoma, multiple eruptive xanthoma in infancy, congenital xanthoma tuberosum, xanthoma naeviforme and juvenile giant-cell granuloma.

What is juvenile xanthogranuloma?

Juvenile xanthogranuloma is a type of non-Langerhan's cell histiocytosis (Class IIb). It presents as skin lesions predominantly in infants and young children, more often males, and is present at birth in 20% of cases. However, 10% of cases are adults. It is more common in Caucasians than in those of oriental origin. The cause is unknown.

Differential diagnosis of juvenile xanthogranuloma

Juvenile xanthogranuloma is difficult to distinguish from several other conditions.

How are these disorders diagnosed?

Juvenile xanthogranuloma has a characteristic appearance on dermoscopy, known as "setting sun", in which there is a central yellowish area surrounded by reddish periphery.

Treatment of juvenile xanthogranuloma

Unless they occur in the eyes, juvenile xanthogranulomas are harmless growths and shrink then disappear eventually over 2–3 years, usually without scarring.

Introduction

Juvenile xanthogranulomas are rare, benign tumours of histiocytic cells that occur predominantly in infancy and early childhood and spontaneously regress.

History

Normally present before the age of one year, 20% of cases are found at birth. Up to 10% of cases present in adults

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