icd 9 code for pheochromocytoma

ICD 9 Codes: 227.0 , 194.0 , 255.6 High magnification micrograph of a pheochromocytoma, showing the nested arrangement of cells (Zellballen) and stippled chromatin.

Full Answer

What is the ICD 10 code for pheochromocytoma?

ICD10 code of Pheochromocytoma and ICD9 code What is the ICD10 code for Pheochromocytoma? And the ICD9 code for Pheochromocytoma? Previous 3 answers Next ICD-10-CM code for D35.00 (ICD-9-CM code equivalent is …

What are the genetic variants of pheochromocytoma?

Pheochromocytoma. malignant. specified site - see Neoplasm, malignant, by site. unspecified site C74.10. ICD-10-CM Diagnosis Code C74.10. Malignant neoplasm of medulla of unspecified adrenal gland. 2016 2017 2018 2019 2020 2021 2022 Billable/Specific Code. specified site - see Neoplasm, benign, by site.

What is the best diagnosis for pheochromocytoma?

Benign pheochromocytoma Pheochromocytoma, benign Applies To Suprarenal gland ICD-9-CM Volume 2 Index entries containing back-references to 227.0: Adenoma (sessile) (M8140/0) - see also Neoplasm, by site, benign adrenal (cortex) (cortical) (functioning) (M8370/0) 227.0 clear cell type (M8373/0) 227.0 compact cell type (M8371/0) 227.0

What is the PMID for pheochromocytoma with stroke?

Pheochromocytoma is a mostly benign tumor (malignancy rate 10-15%) which arises from chromaffin cells with excessive catecholamine production and secretion. Most tumors are localized in the adrenals but 15-18% of the lesions are found extraadrenally (paragangliomas). Pheochromocytoma is a rare form of secondary hypertension; it can also be ...

Is pheochromocytoma a disease?

Pheochromocytoma is a rare form of secondary hypertension; it can also be found as a feature of familial disease (e.g. von Hippel-Lindau disease, MEN type II) due to genetic mutations of several genes that have been identified recently.

What is the malignancy rate of pheochromocytoma?

Pheochromocytoma is a mostly benign tumor (malignancy rate 10-15%) which arises from chromaffin cells with excessive catecholamine production and secretion. Most tumors are localized in the adrenals but ...

Is a CT scan considered a gold standard?

Abdominal CT scan is still considered the "gold standard" since about 98% of the tumors lie infradiaphragmatically. Magnetic resonance imaging (MRI) and MIBG-scanning are other useful methods. Recently, positron emission tomography (PET) based techniques have also been developed.

What is a pheochromocytoma?

Pheochromocytoma ( PHEO or PCC) is a rare tumor of the adrenal medulla composed of chromaffin cells, also known as pheochromocytes. When a tumor composed of the same cells as a pheochromocytoma develops outside the adrenal gland, it is referred to as a paraganglioma. These neuroendocrine tumors are capable of producing and releasing massive amounts ...

What is the gold standard for pheochromocytoma?

Gold standard. Elevated plasma free metanephrines is considered the gold standard diagnosis for pheochromocytoma. Over 10 studies have confirmed that the sensitivity and specificity of this test is 97% and 93% respectively; however, there is still concern for false positive results in the correct clinical scenario.

What is the best treatment for pheochromocytoma?

Surgical resection is the only curative option for pheochromocytoma as of 2019. A successful excision is a multidisciplinary effort involving the endocrinologist and the patient pre-operatively (discussed below) and the surgical team and anesthesiologist intraoperatively. Without frequent and adequate communication between all of the above mentioned teams, a favorable outcome is much more difficult. The United States Endocrine Society 2014 Clinical Practice Guideline for pheochromocytoma recommend a laparoscopic adrenalectomy (minimally invasive technique) for most adrenal tumors, unless they are invasive or are larger than 6.0 centimeters. It is important to note that larger tumors can be attempted with a minimally invasive approach, but the team should be prepared to convert to an open procedure if necessary. An open procedure (traditional surgical technique) is currently preferred for extra-adrenal disease, unless the tumor is small, non-invasive, and in an easy to maneuver location. While previous data indicated the need for a minimally invasive approach with malignant and/or metastatic disease, current research indicates a successful operation is feasible and results in a shorter hospital stay. Literature within the last decade has also demonstrated that the robotic technique may be successfully utilized for adrenal tumors.

Who is best suited to treat metastatic pheochromocytoma?

Metastatic pheochromocytoma is best managed with a multidisciplinary team of oncologists, surgeons, radiologists, nuclear medicine physicians, and endocrinologists. There are several treatment options available to patients depending on the amount and location of disease:

What are the symptoms of neuroendocrine tumors?

These neuroendocrine tumors are capable of producing and releasing massive amounts of catecholamines, metanephrines, or methoxytyramine, which result in the most common symptoms, including hypertension (high blood pressure), tachycardia (fast heart rate), and diaphoresis (sweating).

Is norepinephrine a catecholamine?

Norepinephrine (a catecholamine) is hypothesized to resulted in damaged cardiac tissue by inhibiting coronary blood flow and depriving cells of oxygen, thus resulting in ischemic tissue. Fortunately, following tumor excision and the subsequent quelling of catecholamines, the damage has been proven reversible.

What are the symptoms of migraines?

While 71% of the studied patients reported headaches, just over 20% of the affected patients endorsed associated nausea, vomiting, photophobia, or phonophobia, which are typically associated with migraines.