icd 9 code for prunce belly syndrome

What is prune belly syndrome?

Prune-Belly syndrome, also known as Eagle-Barrett syndrome, is a rare disorder characterized by partial or complete absence of the stomach (abdominal) muscles, failure of both testes to descend into the scrotum (bilateral cryptorchidism), and/or urinary tract malformations.

Why is it called prune belly syndrome?

Prune belly syndrome is a rare condition that gets its name because weak or absent abdominal wall muscles make an infant's belly look wrinkled.

How do you get prune belly syndrome?

The cause of prune belly syndrome is unknown; however, some cases have been reported in siblings, suggesting there may be a genetic component. Prune belly syndrome develops as the fetus is growing before birth.

Why is it called Eagle-Barrett Syndrome?

In 1901, Osler gave the condition its name, which refers to the wrinkled appearance of the abdomen resulting from the muscular deficiency. Prune belly syndrome is also called Eagle-Barrett syndrome, Obrinsky syndrome, and triad syndrome.

How long do people with prune belly syndrome live?

Some babies who have prune belly syndrome may die in the uterus at 20 weeks of pregnancy or later (stillborn). Some babies with this condition die a few months after birth.

Is prune belly syndrome fatal?

Also referred to as triad syndrome or Eagle-Barrett syndrome, prune belly syndrome is a congenital condition that relates to weakness in the stomach, issues in the testicles and trouble with formation of the urinary system. Prune belly syndrome is very rare, but can be severe and even fatal in some cases.

Can prune belly syndrome be cured?

Renal surgery was performed on 5 patients. Four patients with non-functioning kidneys with hydronephrosis underwent a nephrectomy and one patient pyeloplasty. We demonstrate that successful treatment is possible even in cases of serious and complex malformations, such as those of the Prune-Belly syndrome.

Is prune belly syndrome genetic?

Genetic Disease. Prune belly syndrome is a genetic disease, which means that it is caused by one or more genes not working correctly.

What is a congenital malformation?

Congenital malformations of musculoskeletal system, not elsewhere classified. Clinical Information. A rare congenital syndrome occurring almost exclusively in males. It is characterized by partial or complete lack of the abdominal wall muscles, enlarged bladder, dilated ureters, hydronephrosis, and undescended testes.

What is the term for a thin, wrinkled, and shriveled abdominal wall?

A syndrome of hypoplasia or aplasia of the abdominal muscle, presenting a thin, loose, wrinkled and shriveled (prunelike) abdominal wall, with furrowlike umbilicus, and other anomalies, including persistent urachus, pigeon breast deformity, and a variety of gastrointestinal, cardiovascular, urogenital, and skeletal abnormalities. ...

Can prune belly syndrome be caused by pulmonic stenosis?

Prune belly syndrome may occur with or without pulmonic stenosis, de afness, and mental retardation . Distention of the bladder and urethra in utero is considered as a possible cause of abdominal overdistention. Present On Admission. POA Help.

What is prune belly syndrome?

About 97% of those affected are male. Prune belly syndrome is a congenital disorder of the urinary system, characterized by a triad of symptoms. The syndrome is named for the mass of wrinkled skin that is often (but not always) present on the abdomen of those with the disorder. Specialty:

What is billable code?

Billable codes are sufficient justification for admission to an acute care hospital when used a principal diagnosis. The Center for Medicare & Medicaid Services (CMS) requires medical coders to indicate whether or not a condition was present at the time of admission, in order to properly assign MS-DRG codes.