icd 9 code for tof

What are the differential diagnosis of TOF?

Tetralogy of Fallot is a combination of four congenital heart defects. The four defects are a ventricular septal defect (VSD), pulmonary stenosis, a misplaced aorta and a thickened right ventricular wall (right ventricular hypertrophy). They usually result in a lack of oxygen-rich blood reaching the body.

What is TOF in?

Tetralogy of Fallot (TOF) is a combination of four congenital (present at birth) heart defects that affect infants and children. The defects occur together and change the way blood flows through the heart and lungs. TOF occurs in about 1 out of every 2,518 babies born in the U.S. each year.

Is TOF a cyanotic heart disease?

Tetralogy of Fallot is the most common form of cyanotic congenital heart disease. Cyanosis is the abnormal bluish discoloration of the skin that occurs because of low levels of circulating oxygen in the blood.

What is a TOF spell?

Information for parents and carers Page 2 Children with TOF may have a period where they become irritable with uncontrolled crying, have rapid and deep breathing and become very blue or pale /grey and floppy. This is called a hypercyanotic episode or 'spell'.

How is TOF diagnosed?

Tetralogy of Fallot may be diagnosed with fetal echocardiogram (ultrasound) before your baby is born. Our Fetal Heart Program will then prepare a plan for delivery and care immediately after birth. Another common time for diagnosis of tetralogy of Fallot is after birth, but before your newborn leaves the hospital.

What causes tetralogy Fallot?

Tetralogy of Fallot (pronounced te-tral-uh-jee of Fal-oh) is a birth defect that affects normal blood flow through the heart. It happens when a baby's heart does not form correctly as the baby grows and develops in the mother's womb during pregnancy.

What is the ICD 10 code for tetralogy of Fallot?

3: Tetralogy of Fallot.

What does F mean in TOF?

Tetralogy of Fallot (fah-LO) is a congenital (present at birth) heart defect. In tetralogy of Fallot (TOF), four related heart defects change the way blood flows to the lungs and through the heart.

Is tetralogy of Fallot Acyanotic or cyanotic?

Congestive heart failure is the primary concern in infants with acyanotic lesions. The most common cyanotic lesions are tetralogy of Fallot and transposition of the great arteries.

What type of murmur is heard in TOF?

The most common signs and symptoms seen for a newborn with tetralogy of Fallot include: 1) a loud heart murmur (systolic ejection murmur at the left upper sternal border due to pulmonic stenosis and/or holosystolic murmur at the left mid sternal border due to a ventricular septal defect); and 2) cyanosis.

Why does tetralogy of Fallot have a single S2?

The 2nd heart sound (S2) is usually single because the pulmonary component is markedly reduced. A prominent right ventricular impulse and a systolic thrill may be present.

Is a tet spell an emergency?

Tet spell is an episodic central cyanosis due to total occlusion of right ventricle outflow in a patient with a congenital heart disease, such as Tetralogy of Fallot (TOF). There are limited cases of patients who lived with untreated TOF until adulthood. Tet spell in an adult is rarely seen in an emergency department.

What is TOF in surgery?

Open heart surgery. Frequency. 1 in 2,000 babies. Tetralogy of Fallot ( TOF) is a congenital heart defect. Symptoms at birth may vary from none to severe. Later, there are typically episodes of bluish color to the skin known as cyanosis.

How is TOF treated?

TOF is typically treated by open heart surgery in the first year of life. The timing of surgery depends on the baby's symptoms and size. The procedure involves increasing the size of the pulmonary valve and pulmonary arteries and repairing the ventricular septal defect.

What is the prognosis of Fallot?

Prognosis. Untreated, tetralogy of Fallot rapidly results in progressive right ventricular hypertrophy due to the increased resistance caused by narrowing of the pulmonary trunk. This progresses to heart failure which begins in the right ventricle and often leads to left heart failure and dilated cardiomyopathy.

What is the tetralogy of Fallot with pulmonary atresia?

Tetralogy of Fallot with pulmonary atresia ( pseudotruncus arteriosus) is a severe variant in which there is complete obstruction (atresia) of the right ventricular outflow tract, causing an absence of the pulmonary trunk during embryonic development.

What are the four defects of Down syndrome?

It may also be associated with Down syndrome. Classically there are four defects: pulmonary stenosis, narrowing of the exit from the right ventricle. a ventricular septal defect, a hole between the two ventricles. right ventricular hypertrophy, thickening of the right ventricular muscle.

What is the cyanotic range of a baby?

Typical ranges vary from 60% to around 90%. Depending on the degree of obstruction, symptoms vary from no cyanosis or mild cyanosis to profound cyanosis at birth. If the baby is not cyanotic then it is sometimes referred to as a "pink tet".

Is Fallot's tetralogy a secondary anomaly?

This feature is now generally agreed to be a secondary anomaly, as the level of hypertrophy tends to increase with age. Fallot's tetralogy specimen, from the UCT Pathology Learning Centre. There is anatomic variation between the hearts of individuals with tetralogy of Fallot.

What is the ICD code for blue baby syndrome?

The ICD code Q213 is used to code Tetralogy of Fallot. Tetralogy of Fallot (TOF) is a congenital heart defect which is classically understood to involve four anatomical abnormalities of the heart (although only three of them are always present). It is the most common cyanotic heart defect and the most common cause of blue baby syndrome.

What is billable code?

Billable codes are sufficient justification for admission to an acute care hospital when used a principal diagnosis. The Center for Medicare & Medicaid Services (CMS) requires medical coders to indicate whether or not a condition was present at the time of admission, in order to properly assign MS-DRG codes.