Full Answer
Center for Thoracic Insufficiency Syndrome. The vertical expandable prosthetic titanium rib (VEPTR) is the only FDA-approved device to treat children with thoracic insufficiency syndrome, a congenital condition where severe deformities of the chest, spine and ribs prevent normal breathing, lung growth and lung development.
VEPTR is a curved metal rod that is surgically attached to a child’s ribs, spine or pelvis using hooks on both ends of the device. The VEPTR helps straighten the child’s spine and separate ribs so their lungs can grow and expand as the child grows. The length of the VEPTR device can be expanded or contracted as the patient grows.
If your child is diagnosed with thoracic insufficiency syndrome, VEPTR treatment is generally recommended. If your child has a spine disorder, but no related lung or chest issues, VEPTR is generally not an appropriate treatment option. Instead, doctors may recommend other surgical or nonsurgical options to address your child’s condition, such as:
ICD-10-PCS 0PT20ZZ is a specific/billable code that can be used to indicate a procedure.
The vertical expandable prosthetic titanium rib (VEPTR) is the only FDA-approved device to treat children with thoracic insufficiency syndrome, a congenital condition where severe deformities of the chest, spine and ribs prevent normal breathing, lung growth and lung development.
During surgery, doctors attach and adjust the VEPTR device to fit your child. The device is generally attached vertically on your child’s ribs near the spine. In some cases, more than one VEPTR device is used to create space in the chest for the lungs to develop more fully.
Growing use of VEPTR treatment. In the past 20 years, thousands of VEPTRs have been implanted into children in more than 25 countries worldwide. CHOP has been performing VEPTR surgery on children with thoracic insufficiency syndrome for nearly 10 years and has performed hundreds of VEPTR implant and revision surgeries.
The VEPTR helps straighten the child’s spine and separate ribs so their lungs can grow and expand as the child grows. The length of the VEPTR device can be expanded or contracted as the patient grows.
Long-term outcomes for children undergoing VEPTR surgery are generally good. The VEPTR allows your child’s lungs to grow as they grow. When your child reaches skeletal maturity, our team will likely recommend spinal fusion surgery to make the spine and chest wall correction permanent.
Your child — and the device — will need to continue to be monitored, but the VEPTR will continue to act as a replacement rib, ensuring your child’s chest wall remains open, lung volume is maximized, and internal organs are protected.