icd 10 code for rosai dorfman disease

What is the ICD 10 code for Rosai-Dorfman disease?

Oct 01, 2021 · D76.3 is a billable/specific ICD-10-CM code that can be used to indicate a diagnosis for reimbursement purposes. The 2022 edition of ICD-10-CM D76.3 became effective on October 1, 2021. This is the American ICD-10-CM version of D76.3 - other international versions of ICD-10 D76.3 may differ. Applicable To Reticulohistiocytoma (giant-cell)

What is Destombes–Rosai–Dorfman disease?

Destombes-Rosaï-Dorfman disease. Rosaï-Dorfman-Destombes disease. SHML. Sinus histiocytosis with massive lymphadenopathy. Prevalence: Unknown. Inheritance: -. Age of onset: Adolescent, Adult. ICD-10: D76.3. OMIM: -.

What is Rosai-Dorfman disease (RDD)?

Jul 22, 2013 · Rosai-Dorfman disease was first described by Rosai and Dorfman in 1969. It is a benign disease which is characterized by over-production and accumulation of a specific type of white blood cell in the lymph nodes of the body, most often those of the neck (cervical). Other lymph node groups may also be involved and, in some cases, abnormal accumulation of …

What is the prognosis of Rosai-Dorfman disease?

Definition. This is a reactive condition of unknown etiology with increased histiocytes. The disease can mimic lymphoma. Extranodal involvement is frequent. The majority of lesion s are self-limited and benign. Rare fatalities have been associated with immunologic disorder s, lymphoma s of Hodgkin and non-Hodgkin type, leukemia s and ...

What is Rosai-Dorfman syndrome?

General Discussion. Rosai-Dorfman disease is a rare disorder characterized by overproduction (proliferation) and accumulation of a specific type of white blood cell (histiocyte) in the lymph nodes of the body (lymphadenopathy), most often those of the neck (cervical lymphadenopathy).

What causes Rosai-Dorfman disease?

The exact cause of Rosai-Dorfman disease is unknown. Possible causes include altered immune responses and infections by agents such as varicella-zoster and other herpetic viruses ; Epstein-Barr; cytomegalovirus; Brucella; and Klebsiella.

What is unifocal Langerhans Cell Histiocytosis?

Unifocal LCH, also called eosinophilic granuloma (an older term which is now known to be a misnomer), is a disease characterized by an expanding proliferation of Langerhans cells in one organ, where they cause damage called lesions.

How do you treat Rosai-Dorfman disease?

Treatments and overall response rates (ORR) in patients with Rosai-Dorfman disease. Corticosteroids were used as the first-line therapy in 17 (27%) patients. Of these, responses were observed in in 56% of the cases, with a maximum response duration of 71 months and a relapse rate of 53%.Feb 1, 2020

Is Rosai-Dorfman genetic?

Nevertheless, we propose that Rosai–Dorfman disease is a clonal histiocytic disorder driven by genetic alterations, at least in mutated cases, similar to Langerhans cell histiocytosis and other non-Langerhans cell histiocytosis histiocytoses.Jun 30, 2017

Who treats Rosai-Dorfman?

Dr. Vardhana has been practicing medicine for over 22 years and is rated as a Distinguished doctor by MediFind in the treatment of Rosai-Dorfman Disease. He is also highly rated in 23 other conditions, according to our data.

Is Langerhans cell histiocytosis a form of leukemia?

Acute lymphoblastic leukemia is more often associated with LC histiocytosis in children, whereas lymphoma and acute myeloid leukemia are more common in adults, which may reflect the frequency of these diseases in the respective populations.Nov 1, 2013

What is Letterer-Siwe disease?

Letterer–Siwe disease, (LSD) or Abt-Letterer-Siwe disease, is one of the four recognized clinical syndromes of Langerhans cell histiocytosis (LCH) and is the most severe form, involving multiple organ systems such as the skin, bone marrow, spleen, liver, and lung.

Is Langerhans cell histiocytosis an autoimmune disease?

Langerhans cell histiocytosis historically was thought of as a cancer-like condition, but more recently researchers have begun to consider it an autoimmune phenomenon in which immune cells begin to overproduce and attack the body instead of fighting infection.

What is RD diagnosis?

Rosai-Dorfman disease (RD), also known as sinus histiocytosis with massive lymphadenopathy (SHML), is a rare histiocytic disorder which involves the over-production of a type of white blood cell called non Langerhans sinus histiocyte.

What is Rosai Dorfman disease?

It is a benign disease which is characterized by over-production and accumulation of a specific type of white blood cell ( histiocyte) in the lymph nodes of the body, most often those of the neck (cervical). [2] . Other lymph node groups may also be involved and, in some ...

How long does Rosai Dorfman disease last?

In many cases, the signs and symptoms of Rosai-Dorfman disease go away without any treatment (spontaneous remission) within months or a few years. When possible, the preferred course of management is continuous observation without treatment.

What is the HPO database?

People with the same disease may not have all the symptoms listed. This information comes from a database called the Human Phenotype Ontology (HPO) . The HPO collects information on symptoms that have been described in medical resources.

What is a registry?

A registry supports research by collecting of information about patients that share something in common, such as being diagnosed with Rosai-Dorfman disease. The type of data collected can vary from registry to registry and is based on the goals and purpose of that registry.

What is support and advocacy?

Support and advocacy groups can help you connect with other patients and families, and they can provide valuable services. Many develop patient-centered information and are the driving force behind research for better treatments and possible cures. They can direct you to research, resources, and services.

What is monarch tool?

Monarch’s tools are designed to make it easier to compare the signs and symptoms (phenotypes) of different diseases and discover common features. This initiative is a collaboration between several academic institutions across the world and is funded by the National Institutes of Health.

Why is research important?

Research helps us better understand diseases and can lead to advances in diagnosis and treatment. This section provides resources to help you learn about medical research and ways to get involved.

What is the ICD10 code for Rosai-Dorfman disease? And the ICD9 code for Rosai-Dorfman disease?

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What is the history of Rosai-Dorfman disease?

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